Liver transplant for adult hemophagocytic lymphohistiocytosis: case report and literature review.
نویسندگان
چکیده
We report the case of a middle-aged man who died from multiorgan failure 3 weeks after orthotopic liver transplant for fulminant hepatic failure, associated with a rare, often fatal, hematologic condition that usually presents in childhood. We discuss the importance of its diagnosis, treatment, and implications for liver transplant.
منابع مشابه
Hemophagocytic lymphohistiocytosis after lung transplant: report of 2 cases and a literature review.
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متن کاملمعرفی یک مورد شیرخوار 50 روزه با بیماری لنفوهیستیوسیتوزیس هموفاگوسیتیک و علایم نارسایی کبدی
Expression of Hemophagocytic Lymphohistiocytosis with Hepatic Dysfunction in a 50 days Old Infant L. Borjian MD , H. Nazmieh MSc Received: 27/03/07 Sent for Revision: 13/06/07 Received Revised Manuscript: 08/07/07 Accepted: 26/07/07 Background and Objective: The Hemophagocytic Lymphohistiocytosis (HLH) is a rare disease with the pathologic hallmark of having aggressive proliferation o...
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ورودعنوان ژورنال:
- Experimental and clinical transplantation : official journal of the Middle East Society for Organ Transplantation
دوره 10 5 شماره
صفحات -
تاریخ انتشار 2012